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KMID : 0356920090570030376
Korean Journal of Anesthesiology
2009 Volume.57 No. 3 p.376 ~ p.380
Respiratory failure due to myotonic dystrophy combined with peripartum cardiomyopathy - A case report -
Shim Haeng-Seon

Lee Seong-Ho
Kim In-Kyu
Shin Myoung-Keun
Cho Jin-Yong
Abstract
Myotonic dystrophy is an autosomal-dominant inherited neuromuscular disorder that¡¯s characterized by slowly progressive muscular dystrophy, muscle weakness and myotonia. The clinical features may vary from just cataracts to involvement of multiple organ systems such as various muscles, the heart, lung and intestine. Its most common complication is postoperative respiratory failure. We encountered a patient who developed sudden unexpected peripartum cardiomyopathy (PPCM) and respiratory failure due to presumed myotonic dystrophy after cesarean section. We report here on our clinical experience with this malady and we include a brief review of the medical literature on myotonic dystrophy.
KEYWORD
Myotonic dystrophy, Peripartum cardiomyopathy, Respiratory failure
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